A BIOCHEMICAL AND MOLECULAR BIOLOGY STUDY OF THE CARNITINE ACYLCARNITINE TRANSLOCASE DEFICIENCY DISEASE: A METABOLIC, GENETIC SYNDROME CLINICALLY SIMILAR TO THE CARNITINE PALMITYLTRANSFERASE DEFICIENCY
- 2 Anni 1993/1995
 - 61.975€ Totale Fondi
 
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Pubblicazioni Scientifiche
- 1994 FEBS LETTERS 
MITOCHONDRIAL CARRIER PROTEINS
 - 1995 EUROPEAN JOURNAL OF BIOCHEMISTRY 
PROBING THE ACTIVE-SITE OF THE RECONSTITUTED CARNITINE CARRIER FROM RAT-LIVER MITOCHONDRIA WITH SULFHYDRYL-REAGENTS - A CYSTEINE RESIDUE IS LOCALIZED IN OR NEAR THE SUBSTRATE-BINDING SITE
 - 1995 METHODS IN ENZYMOLOGY 
Mitochondrial metabolite carrier proteins: Purification, reconstitution, and transport studies
 - 1994 BIOCHIMICA ET BIOPHYSICA ACTA-BIOMEMBRANES 
THE RECONSTITUTED CARNITINE CARRIER FROM RAT-LIVER MITOCHONDRIA - EVIDENCE FOR A TRANSPORT MECHANISM DIFFERENT FROM THAT OF THE OTHER MITOCHONDRIAL TRANSLOCATORS
 - 1994 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS 
KINETIC CHARACTERIZATION OF THE RECONSTITUTED ORNITHINE CARRIER FROM RAT-LIVER MITOCHONDRIA